Case Example 2 (Primary Site and Histology)

Patient was found to have multiple markedly avid lymphadenopathy throughout neck, chest, abdomen and pelvis on PET. No other disease seen. FNA/Core biopsy right axillary lymph node positive for Rosai-Dorfman disease.

Involvement Comments
Lymph nodes Lymphadenopathy throughout neck, chest, abdomen and pelvis
Organ involvement None seen
Common metastatic sites None seen

Coding of the case (HemeRetic schema)

Data Item Coding
M Rule M2: Single histology
PH Rule PH21: Multiple lymph node regions
Primary site C778: Multiple lymph nodes
Histology 9749/3: Rosai Dorfman Disease
Diagnostic confirmation 1 (positive histology)
EOD Primary Tumor 100 (limited to lymph nodes)
EOD Regional Nodes 888 (not applicable)
EOD Mets 88 (not applicable)
Summary Stage 1 (limited to lymph nodes)
Mets at Dx Data Items (all 6) Mets at Dx-Distant Lymph Nodes: 8, remaining mets at dx data items: 0 (no involvement)

Updated: December 2, 2025