Case Example 4 (Primary Site and Histology)

Double lung transplant prior to ENT finding nasopharyngeal mass, biopsy path diagnosis "post-transplant lymphoproliferative disorder.” PET work-up neg lad, no other sites of disease, no heme malignancy simultaneously diagnosed. Patient completed 8 cycles of rituximab with repeat PET showing a complete response.

Involvement	Comments
Lymph nodes	None seen
Organ involvement	Nasopharynx: based on the ENT findings
Common metastatic sites	None seen

Coding of the case (HemeRetic schema)

Data Item	Coding
M Rule	M2: Single histology
PH Rule	PH30: Use the Heme DB This is the rule that will direct you to the Hematopoietic Database, but as stated prior, start with the hematopoietic database
Primary site	C119: Nasopharynx, NOS
Histology	9971/3: PTLD
Diagnostic confirmation	1 (positive histology)
EOD Primary Tumor	200 (confined to extralymphatic site)
EOD Regional Nodes	888 (not applicable)
EOD Mets	88 (not applicable)
Summary Stage	1 (confined to extralymphatic site)
Mets at Dx Data Items (all 6)	0 (no involvement)

Updated: December 2, 2025