Chronic Myeloproliferative Disorder

(In ICD-O-3, behavior will change from /1 to /3 and these cases will be reportable)

9950/3 Polycythemia vera (PV, P. vera)

Definition

Overproduction of erythrocytes/red blood cells

ICD-9 code

238.4

Synonyms

  • Polycythemia rubra vera
  • Proliferative polycythemia
  • Chronic erythremia (ICD-9 207.1)
  • Primary polycythemia
  • Splenomegalic polycythemia
  • Vaquez-Osler disease; Osler-Vaquez disease

9960/3 Chronic myeloproliferative disease, NOS

Definition

Overproduction of one or more type of blood cell

ICD-9 code

238.7

Synonym

  • Chronic myeloproliferative disorder

9961/3 Myelosclerosis with myeloid metaplasia

Definition

Condition where bone marrow is initially overactive but then develops fibrosis or scar tissue; term used when myelofibrosis/myelosclerosis is the first disease identified

ICD-9 code

238.7

Synonyms

  • Myelofibrosis as a result of myeloproliferative disease
  • Megakaryocytic myelosclerosis
  • Myelofibrosis (idiopathic) with myeloid metaplasia (AMM)
  • Agnogenic myeloid metaplasia (term commonly used in US; not in ICD-0-3)
  • Primary myelofibrosis (PMF)> See also acute myelofibrosis (9931/3)

9962/3 Essential thrombocythemia

Definition

Overproduction of platelets/thrombocytes resulting in circulatory problems

ICD-9 code

238.7

Synonyms

  • Essential thrombocythemia
  • Essential hemorrhagic thrombocythernia
  • Idiopathic hemorrhagic thrombocythernia
  • Primary thrombocythernia

9863/3 Chronic myelogenous leukemia, NOS