Primary Cutaneous Lymphomas

This schema is for primary cutaneous lymphomas, which like Mycosis Fungoides, originate in the skin. Of the histologies listed, 9597 and 9680 are B-cell lymphomas, while the remaining are T-cell lymphomas. Historically these lymphomas have been included in the general lymphoma grouping.

This schema is for select lymphoma histologies that occur within the skin. EOD Primary Tumor, EOD Regional Nodes, and EOD Mets are all coded.

Staging is based on the number of lesions (single, multiple, contiguous, non-contiguous), peripheral lymph node involvement (these are lymph nodes that are located deep in the subcutaneous tissue and can be palpated if they are enlarged due to tumor), and distant lymph nodes, peripheral blood/bone marrow, or extra-cutaneous (not skin) involvement.

There is one SSDI-PTLD. See Lymphoma for further information

Data Item Criteria/Comments
Histologies 9597, 9680, 9708-9709, 9712, 9718-9719, 9726
Primary Sites C440-C449, C510-C512, C518-C519, C600-C602, C608-C609, C632
EOD Primary Tumor Solitary lesion
Multiple lesions, contiguous sites
Multiple lesions, noncontiguous sites
EOD Regional Nodes Peripheral regional lymph node involvement
EOD Mets Distant lymph nodes
Peripheral blood, bone marrow
Extracutaneous involvement
Summary Stage Code 1: Solitary lesion
Code 2: Multiple lesions, contiguous sites
Code 3: Solitary lesion and peripheral lymph nodes
Code 4: Multiple lesions, contiguous sites, and peripheral lymph nodes
Code 7: Multiple lesions, noncontiguous sites, distant lymph nodes, other mets
PTLD This SSDI, effective for 2025+, collects information on the presence of PTLD with a lymphoma. See Rule M14 and PH1 in the Heme manual

Updated: December 2, 2025